Search results for " iva"
showing 10 items of 60 documents
A new flatworm species of Temnocephala (Rhabdocoela, Temnocephalidae) ectosymbiont on the freshwater crab Valdivia serrata (Decapoda, Trichodactylida…
2020
A new species of temnocephalan is described from the branchial chambers ofValdivia serratain Colombia asTemnocephala ivandarioisp. nov.The most distinctive characters of the new species are in the cirrus and the epidermal ‘excretory’ syncytial plates. In the present study, the terminology to describe the cirrus of species ofTemnocephalais updated. Comparison between the shape of the cirrus of the temnocephalans associated with trichodactylid crabs is also provided.
Vessel shape alterations of the vertebrobasilar arteries in Mucopolysaccharidosis type IVa (Morquio A) patients.
2017
Main symptom of mucopolysaccharidosis type IVa (MPS IVa) is progressive systemic skeletal dysplasia. This is routinely monitored by cerebral and spinal MRI. The vascular system is generally not in the primary focus of interest. In our population of MPS IVa patients we observed vessel shape alterations of the vertebrobasilar arteries, which has not been described before.MRI-datasets of 26 patients with MPS IVa acquired between 2008 and 2015 were eligible for retrospective analysis of the vertebrobasilar arteries. The vessel length and angle of the basilar artery (BA) and both vertebral arteries (VA) were analyzed. A deflection angle between 90° and 130° in the vessel course was defined as to…
Dzejnieku Astrīdes un Ivara Ivasku lasītava
2018
Longitudinal analysis of endurance and respiratory function from a natural history study of Morquio A syndrome
2015
Objectives: Baseline data from the Morquio A Clinical Assessment Program (MorCAP) revealed that individuals with Morquio A syndrome show substantial impairment in multiple domains including endurance and respiratory function (Harmatz et al., Mol Genet Metab, 2013). Here, 1- and 2-year longitudinal endurance and respiratory function data are presented.Methods: Endurance was assessed using the 6-minute walk test (6MWT) and the 3-minute stair climb test (3MSCT). Respiratory function was evaluated by measuring forced vital capacity (PVC) and maximum voluntary ventilation (MW). Data were analyzed using repeated measures ANCOVA models. Annualized estimates of change were determined using model es…
Heterogeneity of Morquio disease.
1986
Further clinical heterogeneity of Morquio disease, mucopolysaccharidosis IV (MPS IV), is delineated by the observation of a 30-year-old man with unusually mild clinical manifestations. He is 156 cm tall, has comparatively mild skeletal abnormalities and fine corneal deposits. Keratosulfaturia is absent. N-Acetylgalactosamine-6-sulfate (GalNAc-6-S) sulfatase (E.C. 3.1.6.-) was markedly reduced in his fibroblasts. The residual enzyme activity exhibited a pH profile comparable to that of patients with the "classical" form of the disorder. From our observation and a review of the literature it is concluded that Morquio disease can be divided in several subgroups: besides the severe ("classical"…
Development and testing of new screening method for keratan sulfate in mucopolysaccharidosis IVA.
2004
Mucopolysaccharidosis IVA (MPS IVA), a progressive lysosomal storage disease, causes skeletal dysplasia through excessive storage of keratan sulfate (KS). We developed an ELISA-sandwich assay that used a MAb specific to KS. Forty-five blood and 59 urine specimens from MPS IVA patients (ages 1–65 y) were analyzed to determine whether KS concentration is a suitable marker for early diagnosis and longitudinal assessment of disease severity. Blood specimens were obtained from patients categorized as phenotypically severe (n = 36) and milder (n = 9). Urine specimens were also analyzed from patients categorized as severe (n = 56) and milder (n = 12), respectively. Blood KS levels (101–1525 ng/mL)…
Kino vakars “Atmiņas par Astrīdi Ivasku”
2017
Rakstā sniegta informācija par Astrīdie Ivaskai (1926–2015), latviešu dzejniecei, kas bijusi gan bibliotekāre, gan skolotāja, gan žurnāliste, veltīto kinovakaru LU Bibliotēkā.
CAP et BEP : une insertion typée selon la spécialité
1995
International audience; Toutes les études consacrées à l'insertion s'accordent à reconna\ⁱtre que les itinéraires des jeunes sont de plus en plus longs et complexes, où alternent périodes de chômage, d'emplois précaires, de stages .. Le risque de chômage s'avère d'autant plus grand que le niveau de formation est faible, l'écart entre sexes est nettement en défaveur des jeunes filles en ce qui concerne l'accès à l'emploi. La dégradation générale du marché du travail a profondément retenti sur la situation des débutants à leur entrée dans la vie active. Pourtant cette détérioration générale renforce les disparités d'insertion selon le niveau de formation, la spécialité suivie et la région de …